Journal of Inherited Metabolic Disease 1995-01-01

Immunosuppressive effects of organic acids accumulating in patients with maple syrup urine disease.

M Wajner, J L Schlottfeldt, K Ckless, C M Wannmacher

Index: J. Inherit. Metab. Dis. 18(2) , 165-8, (1995)

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Structure	Name/CAS No.	Molecular Formula	Articles
	D-α-HYDROXYISOVALERIC ACID CAS:17407-56-6	C₅H₁₀O₃
	2-Hydroxy-3-methylbutyric acid CAS:4026-18-0	C₅H₁₀O₃
	(S)-(+)-2-Hydroxy-3-Methylbutyric acid CAS:17407-55-5	C₅H₁₀O₃

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Structural variation governs substrate specificity for organ...
2007-08-17
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Enantiomeric separation and discrimination of 2-hydroxy acid...
2000-03-31
[J. Chromatogr. A. 874(1) , 91-100, (2000)]

Proton HR-MAS NMR spectroscopic characterization of metaboli...
2008-01-01
[Physiol. Chem. Phys. Med. NMR 40 , 67-88, (2008)]

Bacterial expression of catalytically active fragments of th...
1994-10-14
[J. Mol. Biol. 243(1) , 116-22, (1994)]