Journal of Inherited Metabolic Disease 2000-06-01

Characteristic urine organic acid profile in peroxisomal biogenesis disorders.

S H Korman, H Mandel, A Gutman

Index: J. Inherit. Metab. Dis. 23(4) , 425-8, (2000)

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Structure	Name/CAS No.	Molecular Formula	Articles
	D-α-HYDROXYISOVALERIC ACID CAS:17407-56-6	C₅H₁₀O₃
	2-Hydroxy-3-methylbutyric acid CAS:4026-18-0	C₅H₁₀O₃
	DL-p-Hydroxyphenyllactic acid CAS:6482-98-0	C₉H₁₀O₄
	(S)-(+)-2-Hydroxy-3-Methylbutyric acid CAS:17407-55-5	C₅H₁₀O₃
	Azelaic acid CAS:123-99-9	C₉H₁₆O₄

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