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N-乙酰氨基葡萄糖-6-硫酸钠盐

N-乙酰氨基葡萄糖-6-硫酸钠盐结构式
N-乙酰氨基葡萄糖-6-硫酸钠盐结构式
品牌特惠专场
常用名 N-乙酰氨基葡萄糖-6-硫酸钠盐 英文名 n-acetylglucosamine 6-sulfate sodium salt
CAS号 108321-79-5 分子量 323.25300
密度 N/A 沸点 N/A
分子式 C8H14NNaO9S 熔点 N/A
MSDS 美版 闪点 N/A

Purification of a 75 kDa protein from the organelle matrix of human neutrophils and identification as N-acetylglucosamine-6-sulphatase.

Biochem. J. 387 , 841-847, (2005)

A 75 kDa protein was purified to homogeneity from granule extracts of normal human granulocytes using Sephadex G-75 chromatography, Mono-S cation exchange chromatography and chromatofocusing. The protein consisted of one chain with a molecular mass of 75 kDa,...

Genomic basis of mucopolysaccharidosis type IIID (MIM 252940) revealed by sequencing of GNS encoding N-acetylglucosamine-6-sulfatase.

Genomics 81 , 1-5, (2003)

Mucopolysaccharidosis type IIID (MPS IIID; Sanfilippo syndrome type D; MIM 252940) is caused by deficiency of the activity of N-acetylglucosamine-6-sulfatase (GNS), which is normally required for degradation of heparan sulfate. The clinical features of MPS II...

Aryl sulfatase from Naja nigricolis venom: characterization and possible contribution in the pathology of snake poisoning.

J. Biochem. Mol. Toxicol. 17 , 59-66, (2003)

The venom of Naja nigricolis was found to contain a high level of the enzyme aryl sulfatase. The enzyme was isolated from the venom of N. nigriclois and purified to electrophoretic homogeneity by gel chromatography on Sephadex G-100, DEAE-cellulose, and pheny...

A novel loss-of-function mutation in the GNS gene causes Sanfilippo syndrome type D.

Genet. Couns. 20 , 133-139, (2009)

A novel loss-of-function mutation in the GNS gene causes Sanfilippo syndrome type D: Mucopolysaccharidosis type IIID (MIM 252940) is the least common form of the four subtypes of Sanfilippo syndrome. It is an autosomal recessive lysosomal disorder caused by a...