Tiglyl carnitine

Modify Date: 2024-01-10 16:57:39

Use of Tiglyl carnitine

Tiglyl carnitine is found to be associated with celiac disease and mitochondrial acetoacetyl-CoA thiolase (T2) deficiency.

Name	Tiglyl carnitine
Synonym	More Synonyms

Description	Tiglyl carnitine is found to be associated with celiac disease and mitochondrial acetoacetyl-CoA thiolase (T2) deficiency.
Related Catalog	Research Areas >> Metabolic Disease Natural Products >> Others
Target	Human Endogenous Metabolite
References	[1]. Fukao T, et al. The mitochondrial acetoacetyl-CoA thiolase (T2) deficiency in Japanese patients: urinary organic acid and blood acylcarnitine profiles under stable conditions have subtle abnormalities in T2-deficient patients with some residual T2 activity. J Inherit Metab Dis. 2003;26(5):423-31.

1-Propanaminium, 3-carboxy-N,N,N-trimethyl-2-[[(2E)-2-methyl-1-oxo-2-buten-1-yl]oxy]-, inner salt, (2R)-

O-tiglyl-L-carnitine

(3R)-3-{[(2E)-2-Methyl-2-butenoyl]oxy}-4-(trimethylammonio)butanoate