N-Acetyl-D-galactosamine-6-O-sulphatesodiumsalt
N-Acetyl-D-galactosamine-6-O-sulphatesodiumsalt结构式
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常用名 | N-Acetyl-D-galactosamine-6-O-sulphatesodiumsalt | 英文名 | N-Acetyl-D-galactosamine-6-O-sulphatesodiumsalt |
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| CAS号 | 204575-07-5 | 分子量 | 323.25300 | |
| 密度 | N/A | 沸点 | N/A | |
| 分子式 | C8H14NNaO9S | 熔点 | N/A | |
| MSDS | 美版 | 闪点 | N/A |
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Mucopolysaccharidosis type IVA (Morquio A disease): clinical review and current treatment.
Curr. Pharm. Biotechnol. 12 , 931-945, (2011) Mucopolysaccharidosis IVA (MPS IVA), also known as Morquio A, is a rare, autosomal recessive disorder caused by a deficiency of the lysosomal enzyme N-acetylgalatosamine-6-sulfate-sulfatase (GALNS), which catalyzes a step in the catabolism of glycosaminoglyca... |
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Human N-acetylgalactosamine-4-sulphate sulphatase. Purification, monoclonal antibody production and native and subunit Mr values.
Biochem. J. 248 , 755-764, (1987) Initial purification of N-acetylgalactosamine-4-sulphate sulphatase from human liver homogenates containing approx. 1 mg of enzyme in 26 g of soluble proteins was achieved by a six-column chromatography procedure and yielded approx. 40 micrograms of a single ... |
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N-acetylgalactosamine-6-sulfate sulfatase in human placenta: purification and characteristics.
J. Biochem. 110 , 965-970, (1991) N-Acetylgalactosamine-6-sulfate sulfatase from human placenta was purified 33,600-fold using beta-N-acetyl-D-galactosamine 6-sulfate-(1----4)-beta-D-glucuronic acid-(1----3)-N-acetyl-D-[3H]galactosaminitol 6-sulfate as the substrate. This enzyme is an oligome... |
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Human liver N-acetylgalactosamine 6-sulphatase. Purification and characterization.
Biochem. J. 279 , 515-520, (1991) Human N-acetylgalactosamine 6-sulphatase (EC 3.1.6.14), which is involved in the lysosomal degradation of the glycosaminoglycans keratan sulphate and chondroitin 6-sulphate, was purified more than 130,000-fold in 2.8% yield from liver by an eight-step column ... |
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Polymorphisms in Tunisian patients with N-acetylgalactosamine-6-sulfate sulfatase gene deficiency: implication in Morquio A disease.
Diagn. Pathol. 6 , 11, (2011) Mucopolysaccharidosis type IVA or Morquio A syndrome is characterized by the lack of N-acetylgalactosamine-6-sulfate-sulfatase and the accumulation of keratan sulfate and chondroitin-6-sulfate in the lysosomes. At least, 148 mutations and 16 polymorphisms wer... |